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Images in Clinical Practices

Indian Pediatrics 1999; 36:91 

Sturge Weber Syndrome



An II-year-old boy presented with a sudden onset of left sided hemiparesis. He had a similar episode 5 years back preceded by left sided focal convulsions. The hemiparesis recovered within a few months. He was studying in 6th standard and his school performance was satisfactory.
 
 

Fig. I. Close up of the face showing a capillary hemangioma on the right forehead extending from below the hairline, involving the upper part of right eyebrow and going up to the right side of the nasolabial fold.


His growth and development was also normal. On examination he had a capillary hemangioma involving the right side of forehead and upper eyelid, measuring 8 cm x 5 cm (Fig. 1) and left sided upper motor neuron palsy involving the face, upper limb and lower limb. Rest of the examination was within normal limits. X-ray skull revealed doubtful rail track calcification in the occipital area. CT Scan revealed unilateral right parieto-occipital tram like and serpentine calcification following convolutions suggestive of a calcified cerebral hemangioma (Fig. 2).

 

Fig. 2. Magnified view of the CT scan showing unilateral right parietocciptal tram like and serpentine calcification following convolutions in the supratentorial compartment.


 
Pushpa Chaturvedi, Pradeep Sahare,
Nandkumar Banait,
Kasturba Hospital,
MG1MS Sevagram,
Wardha 442102,
Maharashtra, India.

 

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